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Atypical haemolytic uremic syndrome complicated by microangiopathic antiphospholipid-associated syndromeMeglič, Anamarija ...A 4-year-old boy with an atypical course of haemolytic uremic syndrome (HUS), who developed microangiopathic antiphospholipid-associated syndrome (MAPS) with signs of multiple organ failure during ... the course of his disease, is reported. Early and aggressive treatment with intravenous gammaglobulin, pulsemethylprednisolone and plasmapheresis resulted in an excellent clinical recovery. Our patient showed a concomitant presence of multiple factors that could precipitate atypical HUS, including positive antiphospholipid antibodies, decreased level of factor H and positive anti-ADAMTS-13 antibodies. We suggest that, along with infections, autoimmune conditions or defined genetic abnormalities of complement regulatory genes, MAPS should be considered among the pathogenic mechanisms in patients with atypical HUS.Vir: Lupus. - ISSN 0961-2033 (Letn. 17, št. 9, 2008, str. 842-845)Vrsta gradiva - članek, sestavni delLeto - 2008Jezik - angleškiCOBISS.SI-ID - 24676313
Avtor
Meglič, Anamarija |
Grosek, Štefan |
Benedik-Dolničar, Majda |
Avčin, Tadej
Teme
Hemolytic-Uremic Syndrome |
Therapy |
Diagnosis |
Antiphospholipid Syndrome |
Vasculitis |
Thrombocytopenia |
Thrombosis |
Child, Preschool |
Methylprednisolone |
Gamma-Globulins |
Plasmapheresis |
Antifosfolipidni sindrom |
Hemolitična-uremija, sindrom |
Vaskulitis |
Trombocitopenija |
Tromboza |
Otrok predšolski |
Gama-globulini |
Plazmafereza |
Metilprednizolon
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Povezave do osebnih bibliografij avtorjev | Povezave do podatkov o raziskovalcih v sistemu SICRIS |
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Meglič, Anamarija | 14276 |
Grosek, Štefan | 06756 |
Benedik-Dolničar, Majda | 03564 |
Avčin, Tadej | 19258 |
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