Granular cell tumor in an uncommon tumor that usually appears as a solitary small nodular growth and has a benign course. It is usually located in the head and neck ; it is rarely described in the abdominal wall. We report a rare case of granular cell tumor in the external oblique muscle of the abdominal wall. A 57-year-old woman presented with a non-tender, hard mass in the left lower abdominal wall. She underwent a wide excision of the lesion, which measured 5×4 cm. Histological examination confirmed a granular cell tumor with atypia, and the surgical margins were negative. Ten months after surgery, she noted two recurrent masses at the site of the primary tumor and underwent en-bloc excision of these lesions. Three years after re-excision, she was doing well and free of recurrence.