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Lougaris, Vassilios; Pession, Andrea; Baronio, Manuela; Soresina, Annarosa; Rondelli, Roberto; Gazzurelli, Luisa; Benvenuto, Alessio; Martino, Silvana; Gattorno, Marco; Biondi, Andrea; Zecca, Marco; Marinoni, Maddalena; Fabio, Giovanna; Aiuti, Alessandro; Marseglia, Gianluigi; Putti, Maria Caterina; Agostini, Carlo; Lunardi, Claudio; Tommasini, Alberto; Bertolini, Patrizia; Gambineri, Eleonora; Consolini, Rita; Matucci, Andrea; Azzari, Chiara; Danieli, Maria Giovanna; Paganelli, Roberto; Duse, Marzia; Cancrini, Caterina; Moschese, Viviana; Chessa, Luciana; Spadaro, Giuseppe; Civino, Adele; Vacca, Angelo; Cardinale, Fabio; Martire, Baldassare; Carpino, Luigi; Trizzino, Antonino; Russo, Giovanna; Cossu, Fausto; Badolato, Raffaele; Pietrogrande, Maria Cristina; Quinti, Isabella; Rossi, Paolo; Ugazio, Alberto; Pignata, Claudio; Plebani, Alessandro
Journal of clinical immunology, 10/2020, Letnik: 40, Številka: 7Journal Article
Primary immunodeficiencies (PIDs) are heterogeneous disorders, characterized by variable clinical and immunological features. National PID registries offer useful insights on the epidemiology, diagnosis, and natural history of these disorders. In 1999, the Italian network for primary immunodeficiencies (IPINet) was established. We report on data collected from the IPINet registry after 20 years of activity. A total of 3352 pediatric and adult patients affected with PIDs are registered in the database. In Italy, a regional distribution trend of PID diagnosis was observed. Based on the updated IUIS classification of 2019, PID distribution in Italy showed that predominantly antibody deficiencies account for the majority of cases (63%), followed by combined immunodeficiencies with associated or syndromic features (22.5%). The overall age at diagnosis was younger for male patients. The minimal prevalence of PIDs in Italy resulted in 5.1 per 100.000 habitants. Mortality was similar to other European registries (4.2%). Immunoglobulin replacement treatment was prescribed to less than one third of the patient cohort. Collectively, this is the first comprehensive description of the PID epidemiology in Italy.
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Dostop do baze podatkov JCR je dovoljen samo uporabnikom iz Slovenije. Vaš trenutni IP-naslov ni na seznamu dovoljenih za dostop, zato je potrebna avtentikacija z ustreznim računom AAI.
Leto | Faktor vpliva | Izdaja | Kategorija | Razvrstitev | ||||
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JCR | SNIP | JCR | SNIP | JCR | SNIP | JCR | SNIP |
Baze podatkov, v katerih je revija indeksirana
Ime baze podatkov | Področje | Leto |
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Povezave do osebnih bibliografij avtorjev | Povezave do podatkov o raziskovalcih v sistemu SICRIS |
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Vir: Osebne bibliografije
in: SICRIS
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