A 67-year-old female was referred to Yokohama City University Hospital because of reccurent intestinal bleeding for two months. Upper gastrointestinal series, endoscopic examination, and abdominal CT ...failed to demonstrate the bleeding CT failed to demonstrate the bleeding site. Selective superior mesenteric arteriography demonstrate the bleeding CT failed to demonstrate the bleeding site. Selective superior mesenteric arteriography malformation was recongnized in the terminal portion of the ileum at laparotomy, and wedge resection was performed. The pathologic study showed a proliferation of the convoluted arteries and veins ranging from mucosal to subserosal layer of the intestine. A rare case of ileal arteriovenous malformation, which was diagnosed by selective arteriographgy, was reported.