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Pfleger, Andreas; Schwinger, Wolfgang; Maier, Alfred; Tauss, Josef; Popper, Helmut H; Zach, Maximilian S
Journal of pediatric hematology/oncology 28, Številka: 4Journal Article
Gorham-Stout syndrome is a rare disease characterized by vascular proliferation in the bones, effecting osteolysis. When it is complicated by chylothorax, the prognosis is poor. The present case illustrates successful management of chylothorax by a combination of surgery (thoracic duct ligation and excision of lymphangiomatous tissue combined with pleurodesis) and treatment with alpha-2b interferon. Treatment in 38 published cases is reviewed.
