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Adaptive skills and mental health in children and adolescents with neuromuscular diseasesGosar, David ...Background Adaptive skills represent the ways that children and adolescents meet their basic needs for self-care, decision making, communication, and learning in their daily life. Having a ... neuromuscular disease (NMD) not only presents mental health issues, but also impacts these skills. Aims Our study aimed to compare the adaptive skills and mental health of paediatric patients with the most common NMDs with their healthy peers and assess how NMDs shape the way patients form relationships with others, engage in leisure activities and take care of their daily living needs. Methods We used the Adaptive Behaviour Assessment System (ABAS-3) and Achenbach Child Behaviour Checklist (CBCL) to compare the adaptive skills and mental health symptoms of 50 NMD patients to a demographically-matched control group of 298 peers. We examined specific outcomes of having myotonic dystrophy (DM), Duchenne muscular dystrophy (DMD), Becker muscular dystrophy (BMD), spinal muscular atrophy (SMA) or a mixed group of other NMDs. Results All NMD patients displayed poor practical adaptive skills. When the disease was more likely to involve the central nervous system (DM, DMD) they also showed additional deficits in their conceptual and social skills. Contrary to previous research no increased rate of psychopathological symptoms was found in NMD patients, with the exception of difficulties in the social domain among patients with DM. Conclusions Although most children with NMDs displayed more limited practical skills, the specific profile of adaptive skills for each patient group needs to be taken into consideration when planning school support and other psychosocial interventions.Vir: European journal of paediatric neurology. - ISSN 1090-3798 (Vol. 30, 2021, str. 134-143)Vrsta gradiva - članek, sestavni del ; neleposlovje za odrasleLeto - 2021Jezik - angleškiCOBISS.SI-ID - 34056451
Avtor
Gosar, David |
Košmrlj, Lejla |
Lešnik Musek, Petra |
Meško, Tamara |
Stropnik, Staša |
Krkoč, Vesna, 1972- |
Golli, Tanja |
Butenko, Tita |
Loboda, Tanja, dr. med. |
Osredkar, Damjan
Teme
neuromuscular disease |
behavioural disorders |
spinal muscular atrophy |
nevromuskularna bolezen |
vedenjske motnje |
mišična atrofija hrbtenice
Vnos na polico
Trajna povezava
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Leto | Faktor vpliva | Izdaja | Kategorija | Razvrstitev | ||||
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JCR | SNIP | JCR | SNIP | JCR | SNIP | JCR | SNIP |
Baze podatkov, v katerih je revija indeksirana
Ime baze podatkov | Področje | Leto |
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Povezave do osebnih bibliografij avtorjev | Povezave do podatkov o raziskovalcih v sistemu SICRIS |
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Gosar, David | 28300 |
Košmrlj, Lejla | |
Lešnik Musek, Petra | 18863 |
Meško, Tamara | |
Stropnik, Staša | 32182 |
Krkoč, Vesna, 1972- | 34232 |
Golli, Tanja | 34992 |
Butenko, Tita | 36552 |
Loboda, Tanja, dr. med. | |
Osredkar, Damjan | 21413 |
Vir: Osebne bibliografije
in: SICRIS
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