Hand Schuller Christian disease Cugati, Goutham; Singh, Manish; Pande, Anil ...
Indian journal of medical and paediatric oncology,
07/2011, Letnik:
32, Številka:
3
Journal Article
Recenzirano
Odprti dostop
A 43-year-old lady presented with progressively increasing multiple swellings over the scalp for two years and increased frequency of micturition and increased water intake for 6 months. There was no ...evidence of other systemic involvement.
Normolipemic plane xanthoma (NPX) is a histiocytic disorder characterized by yellow-orange plaques in the periorbital areas, neck, upper trunk, and flexural folds. Association with systemic disease ...or paraproteinemia has been reported previously, but rarely with Langerhans cell histiocytosis (LCH). We report a case of Hand-Schüller-Christian disease (a type of LCH) in a patient who developed NPX with supraglottic involvement. NPX developed after several courses of chemotherapy and the supraglottic xanthoma occurred about 2 years later. The coexistence of LCH and non-LCH histiocytic lesions in this patient could be a result of chemotherapy-induced changes or may be just coincidental.
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