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Akutna jetrna porfirija pri sladkornem bolniku = Acute hepatic porphyria in diabetic patientLainščak, Mitja ; Kocijančič, BorutAcute hepatic porphyrias are rare disorders of heme metabolism and can potentially be lethal. Diagnosis is based on the clinical presentation and laboratory analysis of urine. Adequate and early ... treatment can prevent furthercomplications. The paper presents a case of a 30-year-old patient with known diabetes mellitus, who had several episodes of abdominal pain over the past three years. During his second hospitalization, acute hepatic porphyria was diagnosed, which was probably due to hypoglycemia and psychological stress. After symptomatic treatment, the patient was discharged with detailed instructions on the factors which may precipitate acute attacks. Upon the outpatient control examination, the patient had no symptoms or clinical or laboratory signs of porphyria. Acute hepatic porphyria is often missed. Normoglycemic patients with diabetes mellitus can have other precipitating factors. Education of patients and prevention of precipitating factors can prevent acute attacks.Vir: Medicinski razgledi : [medicinski pregledni, strokovni in raziskovalni članki]. - ISSN 0025-8121 (Letn. 42, št. 4, 2003, str. 413-417)Vrsta gradiva - članek, sestavni delLeto - 2003Jezik - slovenskiCOBISS.SI-ID - 17661401
Avtor
Lainščak, Mitja |
Kocijančič, Borut
Teme
Porphyria, Hepatic |
Diabetes Mellitus |
Adult |
Precipitating Factors |
Heme |
Biosynthesis |
Abdominal Pain |
Hypoglycemia |
Porphyrins |
Porfirija jetrna |
Sladkorna bolezen |
Hem |
Hipoglikemija |
Odrasli |
Porfirini |
Precipitacijski faktorji |
Trebušna bolečina
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vir: Medicinski razgledi : [medicinski pregledni, strokovni in raziskovalni članki]. - ISSN 0025-8121 (Letn. 42, št. 4, 2003, str. 413-417)
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Lainščak, Mitja | 22680 |
Kocijančič, Borut | 10066 |
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