E-resources
Peer reviewed
Open access
-
Allaer, Laura; Khirani, Sonia; Griffon, Lucie; Massenavette, Bruno; Bierme, Priscille; Aubertin, Guillaume; Stremler, Nathalie; Baravalle-Einaudi, Melisande; Mazenq, Julie; Ioan, Iulia; Schweitzer, Cyril; Binoche, Alexandra; Lampin, Marie Emilie; Mordacq, Clemence; Bergounioux, Jean; Mbieleu, Blaise; Rubinsztajn, Robert; Sigur, Elodie; Labouret, Geraldine; Genevois, Aline; Becourt, Arnaud; Hullo, Eglantine; Debelleix, Stéphane; Galodé, François; Bui, Stéphanei; Moreau, Johan; Renoux, Marie Catherine; Matecki, Stefan; Lubrano Lavadera, Marc; Heyman, Rachel; Pomedio, Michael; Clainche, Laurence Le; Bokov, Plamen; Dudoignon, Benjamin; Masson, Alexandra; Hangard, Pauline; Menetrey, Celine; Jokic, Mikael; Gachelin, Elsa; Perisson, Caroline; Pervillé, Anne; Fina, Agnes; Giovannini-Chami, Lisa; Fleurence, Emmanuelle; Barzic, Audrey; Cros, Pierrick; Breining, Audrey; Ollivier, Morgane; Labbé, Guillaume; Coutier, Laurianne; Taytard, Jessica; Fauroux, Brigitte
Neuromuscular disorders : NMD, 12/2022, Volume: 32, Issue: 11-12Journal Article
•In 2019, 387 children were treated at home with noninvasive ventilation in France.•Most children had spinal muscular atrophy or congenital myopathy/dystrophy.•Ninety-four percent of children were treated with noninvasive ventilation.•Treatment was initiated electively for 85% of children.•Mean objective noninvasive ventilation use was 8.0 ± 3.1 h/night. The aim of the study was to describe the characteristics of children with neuromuscular diseases treated with long term noninvasive ventilation or continuous positive airway pressure in France. On June 1st 2019, 387 patients (63% boys, mean age 11.2 ± 5.5 years) were treated with long term noninvasive ventilation/continuous positive airway pressure. Thirty three percent of patients had spinal muscular atrophy, 30% congenital myopathy/dystrophy, 20% Duchenne muscular dystrophy, 7% Steinert myotonic dystrophy, and 9% other neuromuscular diseases. Ninety-four percent of patients were treated with long term noninvasive ventilation and 6% with continuous positive airway pressure. Treatment was initiated electively for 85% of patients, mainly on an abnormal overnight gas exchange recording (38% of patients). Noninvasive ventilation/continuous positive airway pressure was initiated during a respiratory exacerbation in 15% of patients. Mean duration of noninvasive ventilation/continuous positive airway pressure was 3.3 ± 3.1 years. Mean objective long term noninvasive ventilation/continuous positive airway pressure use was 8.0 ± 3.1 h/24. Spinal muscular atrophy, congenital myopathy/dystrophy, and Duchenne muscular dystrophy represented 83% of children with neuromuscular diseases treated with long term noninvasive ventilation in France. Screening for nocturnal hypoventilation was satisfactory as noninvasive ventilation /continuous positive airway pressure was predominantly initiated electively.
Author
Shelf entry
Permalink
- URL:
Impact factor
Access to the JCR database is permitted only to users from Slovenia. Your current IP address is not on the list of IP addresses with access permission, and authentication with the relevant AAI accout is required.
Year | Impact factor | Edition | Category | Classification | ||||
---|---|---|---|---|---|---|---|---|
JCR | SNIP | JCR | SNIP | JCR | SNIP | JCR | SNIP |
Select the library membership card:
If the library membership card is not in the list,
add a new one.
DRS, in which the journal is indexed
Database name | Field | Year |
---|
Links to authors' personal bibliographies | Links to information on researchers in the SICRIS system |
---|
Source: Personal bibliographies
and: SICRIS
The material is available in full text. If you wish to order the material anyway, click the Continue button.